Suspected congenital pulmonary airway malformation (CPAM/CCAM)
Recommended: Prenatal US + Fetal MRI; postnatal CT Chest is the preferred imaging study for suspected congenital pulmonary airway malformation (cpam/ccam). Cystic / solid lung lesion in neonate.
Recommended study
Prenatal US + Fetal MRI; postnatal CT Chest
Cystic / solid lung lesion in neonate. Stocker classification I-V. Increased risk of infection and rare malignancy (rhabdomyosarcoma).
If the default doesn't apply
Postnatal definitive imaging
CT
CT Chest with IV contrast
IV contrast
Watch-outs
Differentiate from sequestration
Sequestration has systemic arterial supply; image vessels carefully. Hybrid lesions exist.
Surgical resection consideration
Most asymptomatic CPAMs are resected (typically 6-12 months) due to infection / malignancy risk.
Pearls
- Type I (large cysts) most common.
- Type III (microcystic / solid) most severe — fetal hydrops risk.
- Differentiate from congenital diaphragmatic hernia by abdominal contents in chest.